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Meta-Analysis of the Incidence of Liver Cirrhosis Among Patients With a Fontan Circulation

      Over 1.4 million adults in North America are living with congenital heart defects, of whom around 300,000 have severe congenital heart defects, including patients with Fontan physiology. The Fontan circulation is characterized by a high central venous pressure that can lead to back-stream venous congestion affecting vital organs, such as the liver.
      • Gordon-Walker TT
      • Bove K
      • Veldtman G.
      Fontan-associated liver disease: a review.
      Hence, we performed a meta-analysis to estimate the incidence of liver cirrhosis among patients living with a Fontan circulation.
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