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Rupture and dissection of aorta in Marfan's syndrome

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      Abstract

      A case of Marfan's syndrome is presented with autopsy confirmation of rupture and dissection of the thoracic aorta and presence of coarctation of the aorta and patent ductus arteriosus.
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      References

        • Marfan A.B.
        Un cas de déformation congénitale des quatre membres, plus prononcée aux extrémités, charactérisée par l'allongement des os avec un certain degré d'amincissement.
        Bull. et mem. Soc. méd. hôp. Paris. 1896; 13: 220
        • McKusick V.A.
        Heritable disorders of connective tissue: III. The Marfan syndrome.
        J. Chron. Dis. 1955; 2: 609
        • McKusick V.A.
        The cardiovascular aspects of Marfan's syndrome. A heritable disorder of connective tissue.
        Circulation. 1955; 11: 321
        • Piper R.K.
        • Irvine-Jones E.
        Arachnodactylia and its association with congenital heart disease; report of a case and review of the literature.
        Am. J. Dis. Child. 1926; 31: 832
        • Baer R.W.
        • Taussig H.B.
        • Oppenheimer E.H.
        Congenital aneurysmal dilatation of the aorta associated with arachnodactyly.
        Bull. Johns Hopkins Hosp. 1943; 72: 309
        • Etter L.E.
        • Glover L.P.
        Arachnodactyly complicated by dislocated lens and death from rupture of dissecting aneurysm of aorta.
        J. A. M. A. 1943; 123: 88
        • Goyette E.M.
        • Palmer P.W.
        Cardiovascular lesions in arachnodactyly.
        Circulation. 1953; 7: 373
        • Whittaker S.R.F.
        • Sheehan J.D.
        Dissecting aortic aneurysm in Marfan's syndrome.
        Lancet. 1954; 2: 791
        • Uyeyama H.
        • Kondo B.
        • Kamins M.
        Arachnodactylia and cardiovascular disease: Report of an autopsied case with a summary of previously autopsied cases.
        Am. Heart J. 1947; 34: 580
        • Thomas J.
        • Brothers G.B.
        • Anderson R.S.
        • Cuff J.R.
        Marfan's syndrome; a report of three cases with aneurysm of the aorta.
        Am. J. Med. 1952; 12: 613
        • Faivre G.
        • Frenkiel
        • Pernot
        • Hueber
        Le coeur des dépressions sternales congénitales.
        Arch. mal. coeur. 1954; 47: 322
        • Weve H.
        Ueber arachnodaktylia. (Dystrophia mesodermalis congenita, typus Marfan).
        Arch. f. Augenh. 1931; 104: 1
        • Tobin Jr., J.R.
        • Bay E.B.
        • Humphreys E.M.
        Marfan's syndrome in the adult: Dissecting aneurysm of the aorta associated with arachnodactyly.
        Arch. Int. Med. 1947; 80: 475
        • Vejdovsky V.
        Marfan syndrome.
        Lék. Listy. 1946; 1: 539
        • Spickard W.B.
        Arachnodactyly; description of clinical characteristics with report of autopsied case.
        Stanford M. Bull. 1948; 6: 422
        • Lindeboom G.A.
        • Bouwer W.F.
        Dissecting aneurysm (and renal cortical necrosis) associated with arachnodactyly (Marfan's disease).
        Cardiologia. 1949; 15: 12
      1. New England J. Med. 1950; 243: 346
        • Pygott F.
        Arachnodactyly (Marfan's syndrome) with report of two cases.
        Brit. J. Radiol. 1955; 28: 26
        • Moses M.F.
        Aortic aneurysm associated with arachnodactyly.
        Brit. M. J. 1951; 2: 81
        • Macleod M.
        • Williams A.W.
        The cardio-vascular lesions in Marfan's syndrome.
        Arch. Path. 1956; 61: 143
        • Bronson E.
        • Sutherland G.A.
        Ruptured aortic aneurysms in childhood.
        Brit. J. Child. Dis. 1918; 15: 241
        • Austin M.C.
        • Schaefter R.F.
        Marfan's syndrome with unusual blood vessel manifestations.
        Arch. Path. 1957; 64: 205
        • Neilson C.H.
        • Sullivan J.J.
        Dissecting aneurysm of aorta associated with Marfan's syndrome.
        M. J. Australia. 1956; 43: 925
        • Carpent G.
        • Enderle J.
        • Duret R.
        Syndrome de Marfan et aneurysme, dissequant de l'aorte thoracique.
        Acta cardiol. 1956; 11: 384
        • Hirs A.E.
        • Bailey H.L.
        Arachnodactyly associated with healed dissecting aneurysm.
        Calif. Med. 1956; 84: 355
        • Erdheim J.
        Mcdionecrosis aortae idiopathica.
        Arch. Path. Anal. 1929; 273: 454
        • Rottino A.
        Medial degeneration of the aorta as seen in twelve cases of dissecting aneurysm.
        Arch. Path. 1939; 28: 1
        • Rottino A.
        Medial degeneration of the aorta; a study of two hundred and ten routine specimens by a serial block method.
        Arch. Path. 1939; 28: 377
        • Levine E.A.
        • Stein M.
        • Gordon G.
        • Mitchell N.
        Chronic dissecting aneurysm of aorta resembling chronic rheumatic heart disease.
        New England J. Med. 1951; 244: 902